Brand: | Abnova |
Reference: | H00002717-D01 |
Product name: | GLA MaxPab rabbit polyclonal antibody (D01) |
Product description: | Rabbit polyclonal antibody raised against a full-length human GLA protein. |
Gene id: | 2717 |
Gene name: | GLA |
Gene alias: | GALA |
Gene description: | galactosidase, alpha |
Genbank accession: | NM_000169.1 |
Immunogen: | GLA (NP_000160.1, 1 a.a. ~ 429 a.a) full-length human protein. |
Immunogen sequence/protein sequence: | MQLRNPELHLGCALALRFLALVSWDIPGARALDNGLARTPTMGWLHWERFMCNLDCQEEPDSCISEKLFMEMAELMVSEGWKDAGYEYLCIDDCWMAPQRDSEGRLQADPQRFPHGIRQLANYVHSKGLKLGIYADVGNKTCAGFPGSFGYYDIDAQTFADWGVDLLKFDGCYCDSLENLADGYKHMSLALNRTGRSIVYSCEWPLYMWPFQKPNYTEIRQYCNHWRNFADIDDSWKSIKSILDWTSFNQERIVDVAGPGGWNDPDMLVIGNFGLSWNQQVTQMALWAIMAAPLFMSNDLRHISPQAKALLQDKDVIAINQDPLGKQGYQLRQGDNFEVWERPLSGLAWAVAMINRQEIGGPRSYTIAVASLGKGVACNPACFITQLLPVKRKLGFYEWTSRLRSHINPTGTVLLQLENTMQMSLKDLL |
Protein accession: | NP_000160.1 |
Storage buffer: | No additive |
Storage instruction: | Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing. |
Quality control testing: | Antibody reactive against mammalian transfected lysate. |
Product type: | Primary antibodies |
Host species: | Rabbit |
Antigen species / target species: | Human |
Reactivity: | Human |
Application image: |  |
Application image note: | GLA MaxPab rabbit polyclonal antibody. Western Blot analysis of GLA expression in HeLa. |
Applications: | WB-Ce,WB-Tr,IP |
Shipping condition: | Dry Ice |
Publications: | Functional and biological studies of α-galactosidase A variants with uncertain significance from newborn screening in Taiwan.Liao HC, Hsu TR, Young L, Chiang CC, Huang CK, Liu HC, Niu DM, Chen YJ. Mol Genet Metab. 2017 Jun 8. [Epub ahead of print] |